Human Alpha-Galactosidase A/GLA ELISA Kit ELISA试剂盒,Human Alpha-Galactosidase A/GLA ELISA Kit/人α-半乳糖苷酶A / GLA ELISA试剂盒-试剂- bio-rad伯乐一级代理 |伯乐Aminex |伯乐电泳槽1658001| 伯乐ddPCR bio-rad授权代理商、biorad伯乐qpcr仪

Human Alpha-Galactosidase A/GLA ELISA Kit ELISA试剂盒,Human Alpha-Galactosidase A/GLA ELISA Kit/人α-半乳糖苷酶A / GLA ELISA试剂盒

2024-10-24

Human Alpha-Galactosidase A/GLA ELISA Kit/人α-半乳糖苷酶A / GLA ELISA试剂盒

货号：EH21RB,EH21RBX5,EH21RBX10

规格：96 Tests,5X96 Tests,10X96 tests

价格：6641,29884,57271

产品类型：Platinum ELISA

品牌：Thermo Fisher

物种：人

宿主：其它

抗体亚型：其它

荧光染料：其它

灵敏度	45 pg/mL
检测范围	45-10,000 pg/mL
样本类型/体积	血清 50 μL 血浆 50 μL 上清液 50 μL
操作时间	1 hr 20 min
测试时间	4 hr 45 min
Homogenous (no wash)	No
批间变异系数（CV）	<12%
批内变异系数（CV）	<10%
仪器设备	Colorimetric Microplate Reader 酶标仪
规格	5 x 96 Tests
组份	- 预包被96孔板 - 标准品 - 测定稀释浓缩液 - 生物素化检测抗体 - SAV-HRP - 洗涤液 - 显色剂 - 终止液 - 胶板盖
储存温度	2-8℃
Protein name	alpha Galactosidase
Protein aliases	Agalsidase, agalsidase alfa, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, alpha-D-galactoside galactohydrolase 1, alpha-gal A, Alpha-galactosidase A, galactosidase, alpha, Melibiase
物种（Tested）	人
试剂盒类型	Sandwich ELISA Kit
标记（染料）	HRP
检测抗体偶联物	Biotin
Gene aliases	GALA, GLA
Gene ID	(Human) 2717
Gene symbol	GLA
UniProt ID	(Human) P06280

Human Alpha-Galactosidase A/GLA quantitates human Alpha-Galactosidase A/GLA in serum, plasma, supernatant. The assay will exclusively recognize both natural and recombinant human Alpha-Galactosidase A/GLA.人α-半乳糖苷酶A / GLA定量测定血清，血浆，上清液中的人α-半乳糖苷酶A / GLA。该检测试剂盒将专门识别天然和重组人α-半乳糖苷酶A / GLA。Target information 靶标信息This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.该基因编码同二聚体糖蛋白，其水解糖脂和糖蛋白的末端α-半乳糖基部分。该酶主要水解神经酰胺三己糖苷，并且可以催化蜜二糖水解为半乳糖和葡萄糖。该基因中的多种突变会影响该酶的合成，加工和稳定性，从而导致法布里病（Fabry病），这是一种罕见的溶酶体贮积病，由无法分解α-D-半乳糖基糖脂部分引起。For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.仅供研究使用。不用于诊断过程。未经明确授权不得转售。

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Human Alpha-Galactosidase A/GLA ELISA Kit ELISA试剂盒,Human Alpha-Galactosidase A/GLA ELISA Kit/人α-半乳糖苷酶A / GLA ELISA试剂盒

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